16q24.3 microdeletion syndrome

ORPHA: 261250

Overview

16q24.3 microdeletion syndrome is a recently described syndrome associated with variable developmental delay, facial dysmorphism, seizures and autistic spectrum disorder.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with 16q24.3 microdeletion syndrome, sourced from HPO and Orphanet clinical annotations.

High foreheadProtruding earAutismWide mouthHigh palatePointed chinSmooth philtrumLong philtrumMicrognathiaOptic nerve hypoplasiaSeizureFrontal bossingHypoplasia of the corpus callosumVentriculomegalyModerate intellectual disabilityPeriventricular heterotopiaColpocephalyCryptorchidismLong faceTriangular faceHearing impairmentPreauricular skin tagChronic otitis mediaAnteverted naresAstigmatismStrabismusVisual impairmentMyopiaUpslanted palpebral fissureNystagmusDelayed speech and language developmentHip dysplasiaVentricular septal defectDilated cardiomyopathyMitral regurgitationThrombocytopeniaDysphagiaHighly arched eyebrowScoliosisKyphosisBiparietal narrowingIncreased mean corpuscular volumeSolitary median maxillary central incisorProximal placement of thumbAbnormal hair patternFeeding difficultiesThick vermilion border

Classification & Codes

Orphanet Code

ORPHA:261250
16q24.3 microdeletion syndrome
OrphanetORPHA:261250
Treatments0 drug(s)
Symptoms on record47 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO