21q22.11q22.12 microdeletion syndrome

ORPHA: 261323

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with 21q22.11q22.12 microdeletion syndrome, sourced from HPO and Orphanet clinical annotations.

ThrombocytopeniaMicrocephalyCoarse facial featuresBulbous noseAtypical behaviorBrachydactylyIntellectual disabilitySeizureAbsent speechFailure to thrive in infancySmall nailAbnormal facial shapeShort statureSleep-wake cycle disturbanceFeeding difficulties in infancyPostnatal growth retardationSevere global developmental delayCamptodactylyClinodactylyThick lower lip vermilionThin upper lip vermilionRound faceHypertelorismSmooth philtrumLow-set earsRecurrent otitis mediaAnteverted naresStrabismusDownslanted palpebral fissuresDental crowdingHyperactivityDry skinSacral dimplePeriorbital hyperpigmentationAgenesis of corpus callosumAtrial septal defectAnemiaDroolingPoor speechHypoplastic nipplesDownturned corners of mouthDelayed skeletal maturationAcromesomeliaBruxismAlmond-shaped palpebral fissureNail dystrophyMicrotiaFloppy infantShort proximal phalanx of the 5th fingerShort proximal phalanx of the 2nd fingerCone-shaped epiphyses of the phalanges of the handMidface retrusionStereotypical body rockingThick vermilion borderShort palpebral fissureInappropriate cryingScaphocephalyTongue thrustingSelf-injurious behavior

Classification & Codes

Orphanet Code

ORPHA:261323
21q22.11q22.12 microdeletion syndrome
OrphanetORPHA:261323
Treatments0 drug(s)
Symptoms on record59 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO