2q33.1 microdeletion syndrome

ORPHA: 251028

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with 2q33.1 microdeletion syndrome, sourced from HPO and Orphanet clinical annotations.

Global developmental delayAbsent speechAbnormality of the dentitionCleft palateHigh palateMicrocephalyMicrognathiaHigh foreheadProminent nasal bridgeHypermetropiaAtypical behaviorAggressive behaviorHypotoniaBilateral talipes equinovarusAbnormal facial shapeDroolingSparse hairDecreased testicular sizeFeeding difficulties in infancySevere intellectual disabilityProminent foreheadSevere global developmental delayNasogastric tube feeding in infancyCryptorchidismMicropenisNarrow mouthPierre-Robin sequenceMacrocephalyNarrow faceLong faceShort philtrumFacial asymmetryLong philtrumAbnormality of the outer earLow-set earsConvex nasal ridgeWide noseShort neckAbnormality of the eyeDeeply set eyeDownslanted palpebral fissuresColobomaDacryocystitisDental crowdingDental malocclusionMicrodontiaRestlessnessEmotional labilitySelf-mutilationOsteopeniaSlender fingerSeizureHypertoniaVentricular septal defectTalipes equinovarusShort footFrontal bossingMorphological central nervous system abnormalityLower limb spasticityBroad-based gaitFine hairPolyphagiaIncreased susceptibility to fracturesGeneralized joint hypermobilityAbnormality of the kneeObstructive sleep apneaLumbar hyperlordosisTibial bowingShort noseExternal genital hypoplasiaAbnormal hip bone morphologyClinodactyly of the 5th fingerRelative macrocephalyFlat occiputAgenesis of permanent teethPostnatal growth retardationBroad halluxBroad thumbAbnormality of upper lip vermillionProminent calcaneusEsodeviationSmall hand

Classification & Codes

Orphanet Code

ORPHA:251028
2q33.1 microdeletion syndrome
OrphanetORPHA:251028
Treatments0 drug(s)
Symptoms on record82 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO