2q37 monosomy

MeSH: C538317ORPHA: 1001

Overview

Deletion 2q37 or monosomy 2q37 is a chromosomal anomaly involving deletion of chromosome band 2q37 and manifests as three major clinical findings: developmental delay, skeletal malformations and facial dysmorphism

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with 2q37 monosomy, sourced from HPO and Orphanet clinical annotations.

Joint hypermobilityRound faceIntellectual disabilityHypotoniaGlobal developmental delayMidface retrusionThin vermilion borderMicrocephalyUnderdeveloped nasal alaeAnteverted naresDeeply set eyeUpslanted palpebral fissureAtypical behaviorEczematoid dermatitisBrachydactylySeizureObesityUmbilical herniaToe syndactylyShort footFrontal bossingSparse scalp hairHighly arched eyebrowSupernumerary nippleDownturned corners of mouthClinodactyly of the 5th fingerShort palmShort statureDepressed nasal bridgeFinger syndactylyWide intermamillary distanceBilateral single transverse palmar creasesShort metacarpalBroad columellaAbnormal cardiovascular system morphologySparse eyebrowSmall handMulticystic kidney dysplasiaMacrocephalyConductive hearing impairmentShort neckAutismCompulsive behaviorsMotor stereotypyCongenital diaphragmatic herniaLaryngomalaciaAbnormal aortic morphologyPyloric stenosisSleep disturbanceNephroblastomaTracheomalaciaAttention deficit hyperactivity disorder

Classification & Codes

MeSH Code

C538317

Orphanet Code

ORPHA:1001
2q37 monosomy
MeSHC538317
OrphanetORPHA:1001
Treatments0 drug(s)
Symptoms on record52 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO