3-hydroxy-3-methylglutaryl-CoA synthase deficiency

MeSH: C567784ORPHA: 35701

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with 3-hydroxy-3-methylglutaryl-CoA synthase deficiency, sourced from HPO and Orphanet clinical annotations.

SeizureAbnormality of metabolism/homeostasisHypoglycemia

Classification & Codes

MeSH Code

C567784

Orphanet Code

ORPHA:35701
3-hydroxy-3-methylglutaryl-CoA synthase deficiency
MeSHC567784
OrphanetORPHA:35701
Treatments0 drug(s)
Symptoms on record3 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO