3-methylglutaconic aciduria

MeSH: C579867ORPHA: 289902

Overview

organic acidemia that is characterized by elevated levels of 3-methylglutaconic acid and 3-methylglutaric acid in the urine

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

MeSH Code

C579867

Orphanet Code

ORPHA:289902
3-methylglutaconic aciduria
MeSHC579867
OrphanetORPHA:289902
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO