3-methylglutaconic aciduria with deafness, encephalopathy, and Leigh-like syndrome

ORPHA: 352328

Overview

3-methylglutaconic aciduria that has material basis in homozygous or compound heterozygous mutation in the SERAC1 gene on chromosome 6q25

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

Orphanet Code

ORPHA:352328
3-methylglutaconic aciduria with deafness, encephalopathy, and Leigh-like syndrome
OrphanetORPHA:352328
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO