8p23.1 microdeletion syndrome

MeSH: C537827ORPHA: 251071

Overview

8p23.1 deletion involves a partial deletion of the short arm of chromosome 8 characterized by low birth weight, postnatal growth deficiency, mild intellectual deficit, hyperactivity, craniofacial abnormalities, and congenital heart defects.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with 8p23.1 microdeletion syndrome, sourced from HPO and Orphanet clinical annotations.

Mild intellectual disabilityGlobal developmental delayIntrauterine growth retardationCryptorchidismHypospadiasHigh palateMicrocephalyEpicanthusMicrognathiaHigh foreheadLow-set earsAbnormal pinna morphologyWide nasal bridgeShort neckAtypical behaviorTapered fingerSeizureGrowth delayAbnormal cardiac septum morphologyWeight lossPoor speechShort noseShort staturePulmonary artery stenosisBiparietal narrowingWide intermamillary distanceAtrioventricular canal defectAttention deficit hyperactivity disorderAbnormal cardiovascular system morphologyEnlarged thoraxThin vermilion borderFull cheeksProminent nasal bridgeStrabismusDeeply set eyeDownslanted palpebral fissuresUpslanted palpebral fissureCongenital diaphragmatic herniaObesityTetralogy of FallotHypertrophic cardiomyopathyPatent ductus arteriosusTransposition of the great arteriesAbnormal aortic morphologyPes planusHypoplastic left ventricleProximal placement of thumbBroad hallux phalanxBroad thumb

Classification & Codes

MeSH Code

C537827

Orphanet Code

ORPHA:251071
8p23.1 microdeletion syndrome
MeSHC537827
OrphanetORPHA:251071
Treatments0 drug(s)
Symptoms on record49 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO