AA amyloidosis
ICD-10: E85ORPHA: 85443
Overview
protein deposition disease
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with AA amyloidosis, sourced from HPO and Orphanet clinical annotations.
FatigueAbnormality of the kidneyProteinuriaNephrotic syndromeAbnormal heart morphologyHypertrophic cardiomyopathyWeight lossMalabsorptionAbnormal EKGAbnormal pulmonary interstitial morphologySensorimotor neuropathyIncreased circulating immunoglobulin concentrationHepatic amyloidosisAlbuminuriaDecreased QRS voltagePeriorbital purpuraElevated circulating NT-proBNP concentrationMonoclonal light chain cardiac amyloidosisRenal interstitial amyloid depositsErectile dysfunctionIncreased circulating troponin I concentrationIncreased circulating troponin T concentrationRenal insufficiencyXerostomiaBruising susceptibilityAbnormal cardiac ventricle morphologyAnemiaDyspneaHepatomegalyObstructive sleep apneaHypoalbuminemiaElevated circulating alkaline phosphatase concentrationAbdominal distentionAbnormal cardiac atrium morphologyPostural hypotension with compensatory tachycardiaReduced factor X activityAutonomic erectile dysfunctionPeripheral neuropathyAbnormal salivary gland morphologyArrhythmiaConstrictive median neuropathyAbnormal autonomic nervous system physiologyPeripheral edemaPulmonary interstitial high-resolution computed tomography abnormalityJaw claudicationNonproductive coughAbnormal P waveHowell-Jolly bodiesMacroglossiaHoarse voiceDysphagiaGastrointestinal hemorrhageGastroparesisAbnormality of the gastrointestinal tract
Classification & Codes
ICD-10 Code
E85Orphanet Code
ORPHA:85443AA amyloidosis
| ICD-10 | E85 |
| Orphanet | ORPHA:85443 |
| Treatments | 0 drug(s) |
| Symptoms on record | 54 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO