acatalasia

ICD-10: E80.3MeSH: D020642ORPHA: 926

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with acatalasia, sourced from HPO and Orphanet clinical annotations.

Reduced circulating catalase activityOral ulcerSevere periodontitisGingival bleedingGingivitisMicrocytic anemiaType II diabetes mellitusOld-aged sensorineural hearing impairmentGangreneVitiligoParkinsonismArteriosclerosisPremature loss of permanent teethPainNeoplasm of the larynxType I diabetes mellitusSchizophrenia

Classification & Codes

ICD-10 Code

E80.3

MeSH Code

D020642

Orphanet Code

ORPHA:926
acatalasia
ICD-10E80.3
MeSHD020642
OrphanetORPHA:926
Treatments0 drug(s)
Symptoms on record17 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
acatalasia | OrphanDrug