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acquired C1 esterase inhibitor deficiency

ICD-10: D84.1MeSH: C538173ORPHA: 91385

Contents

  1. 1. Overview
  2. 2. Available Treatments
  3. 3. Classification & Codes

Overview

Acquired angioedema (AAE) is characterized by the occurrence of transitory and recurrent subcutaneous and/or submucosal edemas resulting in swelling and/or abdominal pain due to an acquired C1 inhibitor (C1-INH) deficiency

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

ICD-10 Code

D84.1

MeSH Code

C538173

Orphanet Code

ORPHA:91385
acquired C1 esterase inhibitor deficiency
ICD-10D84.1
MeSHC538173
OrphanetORPHA:91385
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO