acquired thrombotic thrombocytopenic purpura
MeSH: C536901ORPHA: 93585
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with acquired thrombotic thrombocytopenic purpura, sourced from HPO and Orphanet clinical annotations.
PurpuraThrombocytopeniaMicroangiopathic hemolytic anemiaAnti-ADAMTS13 antibody positivityProteinuriaHematuriaSeizureComaConfusionStrokeMuscle weaknessReticulocytosisFeverSchistocytosisDiarrheaNauseaAbdominal painDyspneaHeadacheArthralgiaHyperbilirubinemiaMyalgiaLow back painUnconjugated hyperbilirubinemiaFatigueReduced haptoglobin levelIncreased circulating lactate dehydrogenase concentrationIntestinal ischemiaIncreased circulating troponin I concentrationDiplopiaCongestive heart failureSudden cardiac deathMyocardial infarctionAcute kidney injuryAphasiaAbnormal EKGIncreased blood urea nitrogenElevated circulating creatinine concentrationArrhythmiaCardiogenic shockChest pain
Classification & Codes
MeSH Code
C536901Orphanet Code
ORPHA:93585acquired thrombotic thrombocytopenic purpura
| MeSH | C536901 |
| Orphanet | ORPHA:93585 |
| Treatments | 0 drug(s) |
| Symptoms on record | 41 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO