acquired von Willebrand syndrome
ORPHA: 99147
Overview
human disease
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with acquired von Willebrand syndrome, sourced from HPO and Orphanet clinical annotations.
Reduced factor VIII activityHematological neoplasmProlonged prothrombin timeReduced von Willebrand factor activityImpaired ristocetin cofactor assay activityAbnormal cardiovascular system morphologyMenorrhagiaEpistaxisGastrointestinal angiodysplasiaHematuriaBruising susceptibilityPulmonic stenosisAortic valve stenosisMitral regurgitationAortic regurgitationNormocytic anemiaHypochromic anemiaSubcutaneous hemorrhagePersistent bleeding after traumaGastrointestinal hemorrhageMelenaHypotensionJoint hemorrhageRefractory anemiaAstheniaMetrorrhagiaIntracranial hemorrhage
Classification & Codes
Orphanet Code
ORPHA:99147acquired von Willebrand syndrome
| Orphanet | ORPHA:99147 |
| Treatments | 0 drug(s) |
| Symptoms on record | 27 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO