Acrocraniofacial dysostosis

MeSH: C536892ORPHA: 949

Overview

rare disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Acrocraniofacial dysostosis, sourced from HPO and Orphanet clinical annotations.

Posteriorly rotated earsCleft palateTurricephalyShort philtrumMicrognathiaAbnormal pinna morphologyProminent nasal bridgeAnteverted naresDownslanted palpebral fissuresTelecanthusPtosisProptosisTapered fingerTriphalangeal thumbAbnormal fingernail morphologyFlared iliac wingAbnormal form of the vertebral bodiesShort staturePreauricular pitAbnormal toenail morphologyShort distal phalanx of fingerShort 1st metacarpalPartial duplication of the distal phalanx of the halluxBroad thumbMicrocephalyHypertelorismSloping foreheadConductive hearing impairmentSensorineural hearing impairmentChoanal atresiaMyopiaLacrimation abnormalityPectus excavatumCraniosynostosisCoxa valgaGenu valgumAbnormal hip bone morphologySpina bifida occultaAbnormality of the middle ear ossiclesAdvanced eruption of teethUlnar deviation of fingerAbnormal incus morphologyAbnormal malleus morphologyAbnormal cardiovascular system morphology

Classification & Codes

MeSH Code

C536892

Orphanet Code

ORPHA:949
Acrocraniofacial dysostosis
MeSHC536892
OrphanetORPHA:949
Treatments0 drug(s)
Symptoms on record44 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO