acute disseminated encephalomyelitis

MeSH: D004673ORPHA: 83597

Overview

encephalomyelitis characterized by inflammation located in brain and located in spinal cord that damages myelin

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with acute disseminated encephalomyelitis, sourced from HPO and Orphanet clinical annotations.

EncephalopathyDiffuse white matter abnormalitiesCNS demyelinationEEG with generalized slow activityAtypical behaviorIrritabilitySeizureAtaxiaMental deteriorationAbnormal cerebellum morphologyFeverNauseaAbnormal basal ganglia morphologyAbnormal spinal cord morphologyCerebral edemaHeadacheAbnormal periventricular white matter morphologyIncreased CSF protein concentrationAbnormal pyramidal signMyelitisAbnormal thalamic MRI signal intensityAbnormal brainstem MRI signal intensityInterictal EEG abnormalityDisseminated viral infectionAnti-myelin oligodendrocyte glycoprotein antibody positivityExcessive daytime somnolenceCSF lymphocytic pleiocytosisVisual lossAggressive behaviorComaHemiparesisConfusionMuscle weaknessVomitingAbnormal speech patternSomatic sensory dysfunctionRespiratory failure requiring assisted ventilationCranial nerve paralysisEEG with focal slow activityAtypical absence status epilepticusEEG with focal spikesEye movement-induced painNuchal rigidityOptic neuritisInvoluntary movementsViral hepatitisDiaphragmatic paralysisHypointensity of cerebral white matter on MRIHerpes simplex encephalitisPost-vaccination measlesPost-vaccination rubellaSevere Epstein Barr virus infectionSevere parainfluenza infection

Classification & Codes

MeSH Code

D004673

Orphanet Code

ORPHA:83597
acute disseminated encephalomyelitis
MeSHD004673
OrphanetORPHA:83597
Treatments0 drug(s)
Symptoms on record53 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO