adult-onset non-insulinoma persistent hyperinsulinemic hypoglycemia

ORPHA: 276608

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with adult-onset non-insulinoma persistent hyperinsulinemic hypoglycemia, sourced from HPO and Orphanet clinical annotations.

AgitationHyperinsulinemic hypoglycemiaHyperinsulinemiaHyperhidrosisPallorIntellectual disabilitySeizureLethargyComaHeadacheTremorTachycardiaHypoketotic hypoglycemiaDrowsinessProgressive neurologic deteriorationFasting hypoglycemiaGeneralized muscle weaknessIncreased body weightPancreatic islet-cell hyperplasiaReactive hypoglycemiaFatigue

Classification & Codes

Orphanet Code

ORPHA:276608
adult-onset non-insulinoma persistent hyperinsulinemic hypoglycemia
OrphanetORPHA:276608
Treatments0 drug(s)
Symptoms on record21 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO