adult-onset Still's disease
MeSH: D016706ORPHA: 829
Overview
rare from of inflammatory arthritis characterized by fevers, rash, and joint pain
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with adult-onset Still's disease, sourced from HPO and Orphanet clinical annotations.
Skin rashPruritusArthritisJoint swellingFeverIncreased total leukocyte countArthralgiaIncreased circulating ferritin concentrationElevated erythrocyte sedimentation rateArthralgia/arthritisErythemaElevated circulating C-reactive protein concentrationIncreased total neutrophil countFatigueSplenomegalyWeight lossAnemiaAbdominal painPleuritisPleural effusionHepatomegalyLymphadenopathyElevated circulating hepatic transaminase concentrationElevated circulating alkaline phosphatase concentrationMyalgiaTransient pulmonary infiltratesGeneralized lymphadenopathyAstheniaPharyngitisPharyngalgiaMaculopapular exanthemaKoebner PhenomenonProteinuriaEncephalopathyPericarditisPancreatitisNauseaAnorexiaRespiratory distressLymphadenitisRheumatoid factor positiveAbnormal circulating lipid concentrationAntinuclear antibody positivityBone marrow hypocellularityInterstitial pneumonitisHepatitisHemophagocytosisElevated circulating aldolase concentrationMyocarditisCartilage destructionConjunctivitisUveitisDisseminated intravascular coagulationAmyloid depositionNon-infectious meningitisEpiscleritis
Classification & Codes
MeSH Code
D016706Orphanet Code
ORPHA:829adult-onset Still's disease
| MeSH | D016706 |
| Orphanet | ORPHA:829 |
| Treatments | 0 drug(s) |
| Symptoms on record | 56 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO