aggressive fibromatosis
ICD-10: D48.1MeSH: D018222ORPHA: 873
Overview
connective tissue benign, locally invasive neoplasm that occurs most often in the abdomen, arms and legs
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with aggressive fibromatosis, sourced from HPO and Orphanet clinical annotations.
HydronephrosisLimitation of joint mobilitySubcutaneous noduleMalabsorptionAbdominal painGastrointestinal hemorrhageOsteolysisArthralgiaAbnormality of the musculatureMyalgiaAbnormal abdominal wall morphologyIntestinal obstructionAbnormal retinal pigmentationNeoplasm of the skinFibromaAbnormality of the upper urinary tractGastrointestinal desmoid tumorChest painSepsisIntestinal polyposis
Classification & Codes
ICD-10 Code
D48.1MeSH Code
D018222Orphanet Code
ORPHA:873aggressive fibromatosis
| ICD-10 | D48.1 |
| MeSH | D018222 |
| Orphanet | ORPHA:873 |
| Treatments | 0 drug(s) |
| Symptoms on record | 20 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO