Andersen-Tawil syndrome

ICD-10: I45.8MeSH: D050030ORPHA: 37553

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Andersen-Tawil syndrome, sourced from HPO and Orphanet clinical annotations.

Joint hypermobilityPeriodic paralysisEpisodic flaccid weaknessAbnormality of the dentitionMicrognathiaProlonged QT intervalAbnormal facial shapeVentricular arrhythmiaShort staturePeriodic hypokalemic paresisHigh palateThin upper lip vermilionHypertelorismFacial asymmetryTriangular faceHypoplasia of the maxillaBroad foreheadLow-set earsBulbous noseWide nasal bridgeOligodontiaDental crowdingIncreased circulating aldosterone concentrationSeizureSpecific learning disabilityGrowth delayDilated cardiomyopathyTorsade de pointesShort footClinodactyly of the 5th toePalpitationsScoliosis2-3 toe syndactylyAbnormal T-waveBidirectional ventricular ectopyProlonged QTc intervalPersistence of primary teethPremature ventricular contractionPolymorphic and polytopic ventricular extrasystolesPeriodic hyperkalemic paralysisAbnormality of dental colorShort palpebral fissureNeurodevelopmental delayProminent U waveScaphocephalyPolymorphic ventricular tachycardiaSmall handRenal hypoplasiaRenal tubular dysfunctionSyncopeMuscle weaknessHeart arrhythmia

Classification & Codes

ICD-10 Code

I45.8

MeSH Code

D050030

Orphanet Code

ORPHA:37553
Andersen-Tawil syndrome
ICD-10I45.8
MeSHD050030
OrphanetORPHA:37553
Treatments0 drug(s)
Symptoms on record52 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO