androgen insensitivity syndrome

ICD-10: E34.5MeSH: D013734ORPHA: 754

Overview

sex differentiation condition involving hormonal resistance due to androgen receptor dysfunction in a karyotypically male person

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Classification & Codes

ICD-10 Code

E34.5

MeSH Code

D013734

Orphanet Code

ORPHA:754
androgen insensitivity syndrome
ICD-10E34.5
MeSHD013734
OrphanetORPHA:754
Treatments0 drug(s)
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
androgen insensitivity syndrome | OrphanDrug