Angelman syndrome due to maternal 15q11q13 deletion

ORPHA: 98794

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Angelman syndrome due to maternal 15q11q13 deletion, sourced from HPO and Orphanet clinical annotations.

EEG abnormalityCessation of head growthSecondary microcephalyEEG with abnormally slow frequenciesNeurodevelopmental delayWide mouthStrabismusWidely spaced teethAutistic behaviorShort attention spanInappropriate laughterHyperactivityHypopigmentation of the skinObesityConstipationPoor suckHypoplasia of the corpus callosumAbnormal speech patternDroolingLower limb hyperreflexiaScoliosisFunctional motor deficitFlat occiputHypopigmentation of hairIris hypopigmentationFloppy infantProtruding tongueSevere intellectual disabilityFeeding difficultiesDelayed myelinationHappy demeanorTongue thrustingAbnormal eating behaviorMandibular prognathiaAtaxiaMyoclonusTremorAbsent speechDysphagiaHeat intoleranceBroad-based gaitGait imbalancePoor speechLimitation of movement at anklesShortened sleep phaseMild microcephalyAbnormality of movementRecurrent hand flappingSeizureGlobal developmental delay

Classification & Codes

Orphanet Code

ORPHA:98794
Angelman syndrome due to maternal 15q11q13 deletion
OrphanetORPHA:98794
Treatments0 drug(s)
Symptoms on record50 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO