antenatal multiminicore disease with arthrogryposis multiplex congenita

ORPHA: 178148

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with antenatal multiminicore disease with arthrogryposis multiplex congenita, sourced from HPO and Orphanet clinical annotations.

CryptorchidismHigh palateDolichocephalyLow-set earsProminent nasal bridgeWebbed neckShort neckSingle transverse palmar creaseFlexion contractureBell-shaped thoraxRespiratory insufficiencyDelayed gross motor developmentScoliosisReduced vital capacityArthrogryposis multiplex congenitaAxial muscle weaknessMinicore myopathyAbnormality of the palpebral fissuresClinodactylyIncreased endomysial connective tissueKyphosis

Classification & Codes

Orphanet Code

ORPHA:178148
antenatal multiminicore disease with arthrogryposis multiplex congenita
OrphanetORPHA:178148
Treatments0 drug(s)
Symptoms on record21 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO