aorto-ventricular tunnel

ORPHA: 3400

Overview

Aorto-ventricular tunnel is a congenital, extracardiac channel which connects the ascending aorta above the sinotubular junction to the cavity of the left, or (less commonly) right ventricle

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with aorto-ventricular tunnel, sourced from HPO and Orphanet clinical annotations.

Aorto-ventricular tunnelVentricular hypertrophyCongestive heart failureAbnormal heart valve morphologyAbnormal aortic morphologyAortic root aneurysmAbnormal coronary artery morphologyHeart murmur

Classification & Codes

Orphanet Code

ORPHA:3400
aorto-ventricular tunnel
OrphanetORPHA:3400
Treatments0 drug(s)
Symptoms on record8 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO