appendix neuroendocrine neoplasm

ORPHA: 100079

Contents

1. Overview
2. Available Treatments
3. Clinical Presentation
4. Classification & Codes

Overview

neoplasm with neuroendocrine differentiation that arises from the appendix. It includes well differentiated neuroendocrine tumors (low and intermediate grade) and poorly differentiated neuroendocrine carcinomas (high grade)

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with appendix neuroendocrine neoplasm, sourced from HPO and Orphanet clinical annotations.

Intestinal carcinoidNausea and vomitingEpisodic abdominal painPoor appetiteFunctional intestinal obstructionMechanical ileusAbdominal colicBowel urgencyAbnormal bowel soundsHypoactive bowel soundsConstipationAnorexiaHepatomegalyChronic noninfectious lymphadenopathyElevated circulating hepatic transaminase concentrationElevated serum acid phosphataseProtracted diarrheaIleal adenocarcinomaAdenocarcinoma of the colonPrimary hypercortisolismPalpitationsAsthmaHypotensionIncreased serum serotoninMidgut malrotationTricuspid stenosisAdrenocorticotropic hormone excessHeart murmurAppendiceal mucinous neoplasmOvarian neoplasm

Classification & Codes

Orphanet Code

ORPHA:100079

appendix neuroendocrine neoplasm

Orphanet	`ORPHA:100079`
Treatments	0 drug(s)
Symptoms on record	30 signs
Status	published

Factual Authority

Last Updated3/20/2026

Clinical DataHPO · Orphanet

Drug DataFDA · EMA · CDSCO