Aromatase deficiency

MeSH: C537436ORPHA: 91

Overview

medical condition

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Aromatase deficiency, sourced from HPO and Orphanet clinical annotations.

OsteopeniaOsteoporosisGrowth delayObesityBone painDelayed epiphyseal ossificationDelayed skeletal maturationGenu valgumHyperlipidemiaMale infertilityEunuchoid habitusFemale infertilityEnlarged polycystic ovariesFemale pseudohermaphroditismInsulin resistanceAcanthosis nigricansHepatic steatosisMacroorchidism, postpubertalGeneralized hirsutismType II diabetes mellitusCryptorchidismAmbiguous genitalia, femaleTall staturePrimary amenorrheaHypergonadotropic hypogonadism

Classification & Codes

MeSH Code

C537436

Orphanet Code

ORPHA:91
Aromatase deficiency
MeSHC537436
OrphanetORPHA:91
Treatments0 drug(s)
Symptoms on record25 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO