atherosclerosis-deafness-diabetes-epilepsy-nephropathy syndrome

ORPHA: 1192

Overview

medical condition

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with atherosclerosis-deafness-diabetes-epilepsy-nephropathy syndrome, sourced from HPO and Orphanet clinical annotations.

Sensorineural hearing impairmentPhotosensitive myoclonic seizureCoronary artery atherosclerosisAnemiaProgressive neurologic deteriorationAbnormality of mitochondrial metabolismShort statureCerebral artery atherosclerosisType I diabetes mellitusCryptorchidismProteinuriaNephrotic syndromeNephropathyHypertensionHypertoniaGait disturbanceTremorLimitation of joint mobilityAbnormal mitral valve morphologyCerebral cortical atrophyHyperlordosisAplasia/Hypoplasia of the cerebellumArterial stenosis

Classification & Codes

Orphanet Code

ORPHA:1192
atherosclerosis-deafness-diabetes-epilepsy-nephropathy syndrome
OrphanetORPHA:1192
Treatments0 drug(s)
Symptoms on record23 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO