atrial septal defect, ostium secundum type

ORPHA: 99103

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with atrial septal defect, ostium secundum type, sourced from HPO and Orphanet clinical annotations.

Left-to-right shuntPalpitationsExertional dyspneaExercise intoleranceFatigueRight atrial enlargementSystolic heart murmurAbnormal mitral valve morphologyCongestive heart failureMitral regurgitationPulmonary arterial hypertensionDyspneaAtrial flutterSupraventricular tachycardiaAtrial fibrillationSupraventricular arrhythmiaRight ventricular dilatationAbnormal left ventricular functionTricuspid regurgitationBreathing dysregulationPedal edemaArrhythmiaFirst degree atrioventricular blockBundle branch blockST segment depressionOrthopneaCyanosisSyncopeStrokeRight ventricular failurePneumoniaTransient ischemic attackRecurrent bacterial infectionsIncreased pulmonary vascular resistanceAirway obstruction

Classification & Codes

Orphanet Code

ORPHA:99103
atrial septal defect, ostium secundum type
OrphanetORPHA:99103
Treatments0 drug(s)
Symptoms on record35 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO