atypical teratoid rhabdoid tumor

ICD-10: C70ORPHA: 99966

Overview

brain cancer that is usually located in the brain, but can occur anywhere in the central nervous system

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with atypical teratoid rhabdoid tumor, sourced from HPO and Orphanet clinical annotations.

HydrocephalusMacrocephalyIrritabilityApathySeizureAtaxiaMuscle weaknessLimitation of joint mobilityNausea and vomitingMigraineCerebral calcificationReduced consciousnessHemiplegia/hemiparesisCranial nerve paralysisCerebral palsyMalignant neoplasm of the central nervous system

Classification & Codes

ICD-10 Code

C70

Orphanet Code

ORPHA:99966
atypical teratoid rhabdoid tumor
ICD-10C70
OrphanetORPHA:99966
Treatments0 drug(s)
Symptoms on record16 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO