autosomal dominant deafness-onychodystrophy syndrome

ORPHA: 79499

Overview

Dominant deafness-onychodystrophy (DDOD) syndrome is a multiple congenital anomalies syndrome characterized by congenital hearing impairment, small or absent nails on the hands and feet, and small terminal phalanges

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with autosomal dominant deafness-onychodystrophy syndrome, sourced from HPO and Orphanet clinical annotations.

Absent fingernailSevere sensorineural hearing impairmentAbnormality of the dentitionOligodontiaTriphalangeal thumbAbsent toenailAplasia/Hypoplasia of the nailsDolichocephalyHigh foreheadAplasia cutis congenitaIntellectual disabilitySeizurePes planusHypoplastic toenailsAbnormal facial shapePoor speechShort thumbAbsent thumbnailAbsent fifth fingernailSmall, conical teeth

Classification & Codes

Orphanet Code

ORPHA:79499
autosomal dominant deafness-onychodystrophy syndrome
OrphanetORPHA:79499
Treatments0 drug(s)
Symptoms on record20 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO