autosomal dominant non-syndromic intellectual disability44

ORPHA: 476126

Overview

autosomal dominant non-syndromic intellectual disability that has material basis in an autosomal dominant mutation of TRIO on chromosome 5p15.2

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with autosomal dominant non-syndromic intellectual disability44, sourced from HPO and Orphanet clinical annotations.

Mild intellectual disabilityGlobal developmental delayPoor speechAbnormality of the dentitionFacial asymmetryMicrognathiaHigh foreheadSynophrysDental crowdingAtypical behaviorAutistic behaviorTapered fingerScoliosisRecurrent infections2-3 toe syndactylyFeeding difficulties in infancyPrimary microcephalyUrinary incontinenceHigh palateEpicanthusLong philtrumStrabismusAmblyopiaEruption failureAggressive behaviorCompulsive behaviorsMotor stereotypySelf-mutilationPectus excavatumAbnormality of the handSeizureSpecific learning disabilityTremorAbsent speechFailure to thriveComplete atrioventricular canal defectPes planusPoor suckGait ataxiaSleep disturbanceKyphosisHypercalcemiaShort noseClinodactyly of the 5th fingerShort palmSecondary microcephalyBorderline intellectual disabilityAttention deficit hyperactivity disorderCongenital ptosisPartial absence of thumbAplasia of the 1st metacarpalGastrostomy tube feeding in infancyUnilateral radial aplasiaChronic constipationSlanting of the palpebral fissure

Classification & Codes

Orphanet Code

ORPHA:476126
autosomal dominant non-syndromic intellectual disability44
OrphanetORPHA:476126
Treatments0 drug(s)
Symptoms on record55 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO