autosomal dominant optic atrophy and cataract

MeSH: C537128ORPHA: 67036

Overview

gene (19q13.32).

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with autosomal dominant optic atrophy and cataract, sourced from HPO and Orphanet clinical annotations.

Visual impairmentOptic atrophyReduced visual acuityCataractCentral scotomaNystagmusAtaxiaCerebellar atrophyAreflexiaPostural tremorUnsteady gaitAreflexia of lower limbsMuscle spasmParesthesiaSomatic sensory dysfunctionPosterior cortical cataractPainTritanomalyBlindnessRed-green dyschromatopsiaAbnormal thumb morphologyReduced tendon reflexesLimited elbow extensionPes cavusResting tremorPositive Romberg signAbsent Achilles reflexLimited wrist movementExtrapyramidal muscular rigidityPosterior subcapsular cataractAnterior cortical cataractCerulean cataractDeviation of the 2nd fingerDyslexiaAnterior subcapsular cataract

Classification & Codes

MeSH Code

C537128

Orphanet Code

ORPHA:67036
autosomal dominant optic atrophy and cataract
MeSHC537128
OrphanetORPHA:67036
Treatments0 drug(s)
Symptoms on record35 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO