autosomal dominant osteopetrosis 2

ORPHA: 53

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with autosomal dominant osteopetrosis 2, sourced from HPO and Orphanet clinical annotations.

MacrocephalyAbnormal metaphysis morphologyArthritisJoint dislocationFrontal bossingBone painOsteomyelitisRecurrent fracturesOsteoarthritisGeneralized osteosclerosisAbnormal metacarpal morphologyAbnormal epiphysis morphologyCranial nerve paralysisMandibular osteomyelitisShort distal phalanx of fingerFacial palsyAvascular necrosisAbnormality of the dentitionOptic atrophyAnemiaScoliosisGenu valgumShort statureFatigueHydrocephalusHearing impairmentBlindnessCarious teethThrombocytopeniaAbnormal leukocyte morphologyHypocalcemiaOsteosclerosis of the base of the skullAbnormality of multiple cell lineages in the bone marrowTooth abscessVisual impairmentCranial nerve compression

Classification & Codes

Orphanet Code

ORPHA:53
autosomal dominant osteopetrosis 2
OrphanetORPHA:53
Treatments0 drug(s)
Symptoms on record36 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO