autosomal dominant striatal neurodegeneration type 1
ORPHA: 228169
Overview
Autosomal dominant striatal degeneration (ADSD) is an adult-onset movement disorder characterized by bradykinesia, dysarthria and muscle rigidity
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with autosomal dominant striatal neurodegeneration type 1, sourced from HPO and Orphanet clinical annotations.
DysarthriaGait disturbanceDysphagiaRigidityBradykinesiaDysdiadochokinesisAbnormality of movement
Classification & Codes
Orphanet Code
ORPHA:228169autosomal dominant striatal neurodegeneration type 1
| Orphanet | ORPHA:228169 |
| Treatments | 0 drug(s) |
| Symptoms on record | 7 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO