autosomal recessive faciodigitogenital syndrome

ORPHA: 1974

Overview

Autosomal recessive facio-digito-genital syndrome is a very rare syndrome including short stature, facial dysmorphism, hand abnormalities and shawl scrotum

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with autosomal recessive faciodigitogenital syndrome, sourced from HPO and Orphanet clinical annotations.

Joint hypermobilityBrachycephalyOverfolded helixProminent nasal bridgeShort footFrontal bossingShort statureOpen biteMicrognathiaWidow's peakUpslanted palpebral fissureHyperextensible skinCoarse hairHypopigmentation of hairDry hairShawl scrotumWide mouthHigh palateEverted lower lip vermilionLong faceHypertelorismTriangular faceLong philtrumPosteriorly rotated earsAnteverted naresLong neckTelecanthusLong palpebral fissureBrachydactylyDeep philtrumShort noseClinodactyly of the 5th fingerFinger syndactylyDown-sloping shoulders

Classification & Codes

Orphanet Code

ORPHA:1974
autosomal recessive faciodigitogenital syndrome
OrphanetORPHA:1974
Treatments0 drug(s)
Symptoms on record34 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO