autosomal recessive progressive external ophthalmoplegia

MeSH: C564926ORPHA: 254886

Overview

Autosomal recessive form of progressive external ophthalmoplegia

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with autosomal recessive progressive external ophthalmoplegia, sourced from HPO and Orphanet clinical annotations.

Mask-like faciesExternal ophthalmoplegiaCardiomyopathyDysphagiaMyopathyRagged-red muscle fibersSensory axonal neuropathyParesthesiaCytochrome C oxidase-negative muscle fibersMitochondrial myopathyPeripheral neuropathyFacial palsyHearing impairmentAbnormal retinal morphologyVisual impairmentPtosisOptic atrophyDepressionAtaxiaHyporeflexiaCerebellar atrophyWeak voiceCerebral atrophyBradykinesiaAction tremorShuffling gaitCogwheel rigidityAbnormal cerebral white matter morphologyParkinsonism with favorable response to dopaminergic medicationAbnormal cerebrospinal fluid morphologyDistal sensory impairmentExercise intoleranceMuscle stiffnessProximal muscle weaknessDyschromatopsiaStooped postureHand muscle weaknessMuscle fiber atrophyOptic neuritisElevated circulating creatine kinase concentrationScapular wingingCognitive impairment

Classification & Codes

MeSH Code

C564926

Orphanet Code

ORPHA:254886
autosomal recessive progressive external ophthalmoplegia
MeSHC564926
OrphanetORPHA:254886
Treatments0 drug(s)
Symptoms on record42 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO