behavioral variant of frontotemporal dementia
ORPHA: 275864
Overview
Behavioral variant of frontotemporal dementia (bv-FTD) is a form of frontotemporal dementia (FTD; see this term), characterized by progressive behavioral impairment and a decline in executive function with frontal lobe-predominant atrophy
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with behavioral variant of frontotemporal dementia, sourced from HPO and Orphanet clinical annotations.
Thickened nuchal skin foldAtypical behaviorHyperoralityRestlessnessAggressive behaviorInappropriate behaviorRestrictive behaviorMotor stereotypyDisinhibitionIrritabilityPersonality changesLack of insightMental deteriorationFrontotemporal dementiaMemory impairmentLoss of speechAphasiaDyscalculiaPoor speechFrontotemporal cerebral atrophyDyslexiaDysgraphiaEcholaliaEmotional dearthPerseverative thoughtAbnormal cerebral white matter morphologyEEG with continuous slow activityAbnormal brain FDG positron emission tomographyCollectionismPsychosisApathyGait disturbanceHyperreflexiaBilateral tonic-clonic seizureAbnormality of extrapyramidal motor functionMutismFasciculationsAstrocytosisUpper motor neuron dysfunctionAbulia
Classification & Codes
Orphanet Code
ORPHA:275864behavioral variant of frontotemporal dementia
| Orphanet | ORPHA:275864 |
| Treatments | 0 drug(s) |
| Symptoms on record | 40 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO