Behçet's disease

MeSH: D001528ORPHA: 117

Overview

rare immune-mediated small-vessel systemic vasculitis in humans

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Behçet's disease, sourced from HPO and Orphanet clinical annotations.

MalabsorptionAnorexiaPleuritisHemoptysisPulmonary infiltratesPleural effusionPulmonary embolismVertigoMemory impairmentDevelopmental regressionInfectious encephalitisIncreased intracranial pressureCerebral ischemiaLymphadenopathyParesthesiaArterial thrombosisCranial nerve paralysisAbnormal pyramidal signAvascular necrosisMyocarditisNon-infectious meningitisOral ulcerPhotophobiaMeningitisArthritisSubcutaneous noduleFeverNausea and vomitingMigraineVasculitisMyalgiaRecurrent aphthous stomatitisFatigueOrchitisPapuleAcneHemiparesisGait disturbanceConfusionAbdominal painGastrointestinal hemorrhageHeadacheSuperficial thrombophlebitisArthralgiaGenital ulcersElevated erythrocyte sedimentation rateVenous thrombosisNongranulomatous uveitisAbnormal blistering of the skinElevated circulating C-reactive protein concentrationPanuveitisErythema nodosumIncreased inflammatory responsePositive pathergy testImmunologic hypersensitivityPustuleEpididymitisRenal insufficiencyRetinopathyCataractBlindnessAtypical behaviorIrritabilityKeratoconjunctivitis siccaSeizureAtaxiaHyperreflexiaAbnormal myocardium morphologyMitral regurgitationMyocardial infarctionAortic regurgitationPericarditisPancreatitisSplenomegalyWeight lossRecurrent feverEndocarditisMyositisOptic neuritisRetrobulbar optic neuritisGangreneGlomerulopathyAA amyloidosisGlomerulonephritisDiarrhea

Classification & Codes

MeSH Code

D001528

Orphanet Code

ORPHA:117
Behçet's disease
MeSHD001528
OrphanetORPHA:117
Treatments0 drug(s)
Symptoms on record85 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO