benign recurrent intrahepatic cholestasis
ORPHA: 65682
Overview
intrahepatic cholestasis characterized by intermittent, recurrent episodes of intrahepatic cholestasis mostly without progression to liver damage or extrahepatic bile duct obstruction
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with benign recurrent intrahepatic cholestasis, sourced from HPO and Orphanet clinical annotations.
Hearing impairmentJaundicePruritusCholelithiasisCirrhosisHepatocellular carcinomaPancreatitisWeight lossNausea and vomitingAbdominal painChronic diarrheaAnorexiaCholestatic liver diseaseElevated circulating hepatic transaminase concentrationAcholic stoolsFatigue
Classification & Codes
Orphanet Code
ORPHA:65682benign recurrent intrahepatic cholestasis
| Orphanet | ORPHA:65682 |
| Treatments | 0 drug(s) |
| Symptoms on record | 16 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO