benign recurrent intrahepatic cholestasis

ORPHA: 65682

Overview

intrahepatic cholestasis characterized by intermittent, recurrent episodes of intrahepatic cholestasis mostly without progression to liver damage or extrahepatic bile duct obstruction

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with benign recurrent intrahepatic cholestasis, sourced from HPO and Orphanet clinical annotations.

Hearing impairmentJaundicePruritusCholelithiasisCirrhosisHepatocellular carcinomaPancreatitisWeight lossNausea and vomitingAbdominal painChronic diarrheaAnorexiaCholestatic liver diseaseElevated circulating hepatic transaminase concentrationAcholic stoolsFatigue

Classification & Codes

Orphanet Code

ORPHA:65682
benign recurrent intrahepatic cholestasis
OrphanetORPHA:65682
Treatments0 drug(s)
Symptoms on record16 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO