Best’s vitelliform macular dystrophy

ORPHA: 1243

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Best’s vitelliform macular dystrophy, sourced from HPO and Orphanet clinical annotations.

Visual impairmentColor vision defectVisual field defectChorioretinal scalloped atrophyCystoid macular degenerationMetamorphopsia

Classification & Codes

Orphanet Code

ORPHA:1243
Best’s vitelliform macular dystrophy
OrphanetORPHA:1243
Treatments0 drug(s)
Symptoms on record6 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO