Bietti crystalline corneoretinal dystrophy

MeSH: C535440ORPHA: 41751

Overview

Human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Bietti crystalline corneoretinal dystrophy, sourced from HPO and Orphanet clinical annotations.

Visual impairmentDecreased light- and dark-adapted electroretinogram amplitudeNyctalopiaConstriction of peripheral visual fieldRetinal pigment epithelial atrophyCrystalline corneal dystrophyChoriocapillaris atrophySubretinal depositsChorioretinal atrophyColor vision defectPigmentary retinopathyCentral scotomaBlindnessLarge central visual field defectSeverely reduced visual acuityRetinal pigment epithelial mottlingCystoid macular edemaRetinal thinning on OCTParacentral scotoma

Classification & Codes

MeSH Code

C535440

Orphanet Code

ORPHA:41751
Bietti crystalline corneoretinal dystrophy
MeSHC535440
OrphanetORPHA:41751
Treatments0 drug(s)
Symptoms on record19 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO