blepharophimosis-intellectual disability syndrome, MKB type

ORPHA: 293707

Overview

The Maat-Kievit-Brunner type of Ohdo syndrome is a rare condition characterized by intellectual disability and distinctive facial features. It has only been reported in males.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with blepharophimosis-intellectual disability syndrome, MKB type, sourced from HPO and Orphanet clinical annotations.

Coarse facial featuresTriangular faceBulbous noseProminent noseBlepharophimosisIntellectual disabilityFloppy infantThick nasal alae

Classification & Codes

Orphanet Code

ORPHA:293707
blepharophimosis-intellectual disability syndrome, MKB type
OrphanetORPHA:293707
Treatments0 drug(s)
Symptoms on record8 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO