Bloch-Sulzberger syndrome

MeSH: D007184ORPHA: 464

Overview

genetic disorder that affects the skin, hair, teeth, nails, and central nervous system

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Bloch-Sulzberger syndrome, sourced from HPO and Orphanet clinical annotations.

Orofacial cleftHearing abnormalityStrabismusKeratitisVisual impairmentCataractAbnormal chorioretinal morphologyRetinal detachmentUveitisMicrophthalmiaRetinal hemorrhageBlue scleraeHypodontiaAbnormal dental enamel morphologyDelayed eruption of teethHyperkeratosisHyperhidrosisSkin rashAbnormality of skin pigmentationHypopigmented skin patchesAbnormal fingernail morphologyIntellectual disabilitySeizureHypotoniaSpasticityGlobal developmental delayGait disturbanceUmbilical herniaAbnormal hair morphologyAlopeciaAbnormal nail morphologyCongestive heart failureHypoplastic fingernailDystrophic toenailBroad nailIncreased total eosinophil countPulmonary arterial hypertensionCerebral cortical atrophyInfectious encephalitisSupernumerary nippleCerebral ischemiaScoliosisOsteolysisSpina bifida occultaAbsent handDeviation of fingerShort statureHemiplegia/hemiparesisSupernumerary ribsAbnormal hand morphologyFinger syndactylyAbnormal dental morphologyAttention deficit hyperactivity disorderIrregular hyperpigmentationRetinal neovascularizationCorneal opacityAbnormal blistering of the skinAbnormal toenail morphologyRidged fingernailErythemaAbnormality of immune system physiologyCamptodactyly of fingerCognitive impairmentAsymmetric growthTelangiectasia of the skinSkin ulcerVerrucae

Classification & Codes

MeSH Code

D007184

Orphanet Code

ORPHA:464
Bloch-Sulzberger syndrome
MeSHD007184
OrphanetORPHA:464
Treatments0 drug(s)
Symptoms on record67 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO