bullous diffuse cutaneous mastocytosis
ORPHA: 280785
Overview
Bullous diffuse cutaneous mastocytosis (BDCM) is a form of diffuse cutaneous mastocytosis (DCM; see this term) characterized by generalized erythroderma and severe blistering associated with the accumulation of mast cells in the skin
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with bullous diffuse cutaneous mastocytosis, sourced from HPO and Orphanet clinical annotations.
PruritusErythrodermaUrticariaProfuse pigmented skin lesionsCardiorespiratory arrestAbnormal blistering of the skinCutaneous mastocytosis
Classification & Codes
Orphanet Code
ORPHA:280785bullous diffuse cutaneous mastocytosis
| Orphanet | ORPHA:280785 |
| Treatments | 0 drug(s) |
| Symptoms on record | 7 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO