CADASIL

MeSH: D046589ORPHA: 1361 Treatment Available

Overview

autosomal dominant cerebrovascular disorder characterized by recurrent subcortical ischemic stroke and cognitive impairment

Available Treatments (1)

DrugFormStatusCountriesLead Time
Cerebrolysin
InjectionAvailable in some countries4

Clinical Presentation

Signs and symptoms associated with CADASIL, sourced from HPO and Orphanet clinical annotations.

LeukoencephalopathyAbnormal cerebral white matter morphologyLacunar strokeMultifocal hyperintensity of cerebral white matter on MRIEmotional labilityApathyStrokeMigraineMigraine with auraTransient ischemic attackCerebral ischemiaCognitive impairmentDepressionDementiaAnxietyDiabetes mellitusHypertensionSeizureSpasticityDysarthriaGait disturbanceConfusionEncephalopathyParkinsonismCerebral hemorrhageDysphagiaIschemic strokeIntracranial hemorrhageHemiplegiaMotor deteriorationMemory impairmentLanguage impairmentLoss of consciousnessRecurrent subcortical infarctsImpaired visuospatial constructive cognitionStress urinary incontinenceBrain atrophyAbnormally slow thought processArterial stenosisAphasia

Classification & Codes

MeSH Code

D046589

Orphanet Code

ORPHA:136
CADASIL
MeSHD046589
OrphanetORPHA:136
Treatments1 drug(s)
Symptoms on record40 signs
Statuspublished

Treatment Summary

Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO