Castleman's disease
ICD-10: D47.Z2MeSH: D005871ORPHA: 160
Overview
lymphoproliferative syndrome characterized by one or more enlarged lymph nodes containing cells with hyaline-vascular, plasmacytic, or mixed appearance microscopically
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with Castleman's disease, sourced from HPO and Orphanet clinical annotations.
LymphadenopathyWeight lossAnemiaAbdominal painFollicular hyperplasiaElevated erythrocyte sedimentation rateElevated circulating C-reactive protein concentrationFatigueConstitutional symptomIncreased circulating interleukin 6 concentrationMediastinal lymphadenopathyJaundiceNausea and vomitingAbdominal distentionGeneralized lymphadenopathyAbnormality of the gastrointestinal tractCoughDecreased mean corpuscular volumeFlank painAbdominal massRenal insufficiencyHematuriaRestrictive cardiomyopathyThrombocytopeniaDyspneaIntestinal obstructionUreteral obstructionMyelofibrosisAnasarca
Classification & Codes
ICD-10 Code
D47.Z2MeSH Code
D005871Orphanet Code
ORPHA:160Castleman's disease
| ICD-10 | D47.Z2 |
| MeSH | D005871 |
| Orphanet | ORPHA:160 |
| Treatments | 0 drug(s) |
| Symptoms on record | 29 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO