cataract-growth hormone deficiency-sensory neuropathy-sensorineural hearing loss-skeletal dysplasia syndrome

ORPHA: 436174

Overview

human disease

Available Treatments (0)

No treatments linked yet

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Clinical Presentation

Signs and symptoms associated with cataract-growth hormone deficiency-sensory neuropathy-sensorineural hearing loss-skeletal dysplasia syndrome, sourced from HPO and Orphanet clinical annotations.

Narrow mouthPrelingual sensorineural hearing impairmentSensorineural hearing impairmentProgressive sensorineural hearing impairmentCataractThick eyebrowDevelopmental cataractDecreased response to growth hormone stimulation testMotor delayHip dislocationShort statureAchalasiaScoliosisSkeletal dysplasiaSpondyloepiphyseal dysplasiaGenu valgumPeripheral neuropathyFasting hypoglycemiaSpinal canal stenosisThoracic kyphoscoliosisPeriarticular subcutaneous nodulesCervical spinal canal stenosisBilateral sensorineural hearing impairmentProminent forehead

Classification & Codes

Orphanet Code

ORPHA:436174
cataract-growth hormone deficiency-sensory neuropathy-sensorineural hearing loss-skeletal dysplasia syndrome
OrphanetORPHA:436174
Treatments0 drug(s)
Symptoms on record24 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO