catecholaminergic polymorphic ventricular tachycardia

ICD-10: I47.2MeSH: D000098850ORPHA: 3286

Overview

disorder characterized by an abnormal heart rhythm (arrhythmia)

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with catecholaminergic polymorphic ventricular tachycardia, sourced from HPO and Orphanet clinical annotations.

Ventricular tachycardiaCardiac arrestPalpitationsVertigoSupraventricular tachycardiaAtrial fibrillationPolymorphic ventricular tachycardiaSyncopeSudden cardiac deathVentricular fibrillation

Classification & Codes

ICD-10 Code

I47.2

MeSH Code

D000098850

Orphanet Code

ORPHA:3286
catecholaminergic polymorphic ventricular tachycardia
ICD-10I47.2
MeSHD000098850
OrphanetORPHA:3286
Treatments0 drug(s)
Symptoms on record10 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO