catecholaminergic polymorphic ventricular tachycardia
ICD-10: I47.2MeSH: D000098850ORPHA: 3286
Overview
disorder characterized by an abnormal heart rhythm (arrhythmia)
Available Treatments (0)
No treatments linked yet
Clinical trials or compassionate use may be available — consult a specialist.
Clinical Presentation
Signs and symptoms associated with catecholaminergic polymorphic ventricular tachycardia, sourced from HPO and Orphanet clinical annotations.
Ventricular tachycardiaCardiac arrestPalpitationsVertigoSupraventricular tachycardiaAtrial fibrillationPolymorphic ventricular tachycardiaSyncopeSudden cardiac deathVentricular fibrillation
Classification & Codes
ICD-10 Code
I47.2MeSH Code
D000098850Orphanet Code
ORPHA:3286catecholaminergic polymorphic ventricular tachycardia
| ICD-10 | I47.2 |
| MeSH | D000098850 |
| Orphanet | ORPHA:3286 |
| Treatments | 0 drug(s) |
| Symptoms on record | 10 signs |
| Status | published |
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO