CEDNIK syndrome

MeSH: C537943ORPHA: 66631

Overview

human disease

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with CEDNIK syndrome, sourced from HPO and Orphanet clinical annotations.

MicrocephalyLong faceHypertelorismProminent nasal bridgeDownslanted palpebral fissuresIntellectual disabilityAtaxiaGlobal developmental delayPoor head controlDiffuse palmoplantar hyperkeratosisIchthyosisAbnormality of eye movementOptic atrophyAbnormal corpus callosum morphologyAreflexiaPachygyriaPolymicrogyriaAbnormality of peripheral nerve conductionPeripheral neuropathyProteinuriaNephrotic syndromeHypogonadismAbnormality of the dentitionDolichocephalyMacrotiaSensorineural hearing impairmentDepressed nasal ridgeAbnormality of the eyeAbnormality of visionSeizureStrokeCongestive heart failureShort stature

Classification & Codes

MeSH Code

C537943

Orphanet Code

ORPHA:66631
CEDNIK syndrome
MeSHC537943
OrphanetORPHA:66631
Treatments0 drug(s)
Symptoms on record33 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO