Cerebrooculonasal syndrome

MeSH: C565313ORPHA: 66625

Overview

Cerebro-oculo-nasal syndrome is a multisystem malformation syndrome that has been reported in about 10 patients. The clinical features include bilateral anophthalmia, abnormal nares, central nervous system anomalies, and neurodevelopmental delay.

Available Treatments (0)

No treatments linked yet

Clinical trials or compassionate use may be available — consult a specialist.

Clinical Presentation

Signs and symptoms associated with Cerebrooculonasal syndrome, sourced from HPO and Orphanet clinical annotations.

Posteriorly rotated earsBrachycephalyHypertelorismBroad foreheadAnophthalmiaUpslanted palpebral fissureBlindnessAbnormal nostril morphologyUnderdeveloped supraorbital ridgesProminent foreheadLarge faceHigh palateEpicanthusLong philtrumMacrotiaSparse eyelashesWidely spaced teethMicrodontiaPostaxial hand polydactylyIntellectual disabilityTessier cleftSolitary median maxillary central incisorHypoplasia of penisAbnormal tragus morphologyAbnormal nervous system morphologySparse eyebrowU-Shaped upper lip vermilion

Classification & Codes

MeSH Code

C565313

Orphanet Code

ORPHA:66625
Cerebrooculonasal syndrome
MeSHC565313
OrphanetORPHA:66625
Treatments0 drug(s)
Symptoms on record27 signs
Statuspublished
Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO
Cerebrooculonasal syndrome | OrphanDrug