Charcot-Marie-tooth disease-deafness-intellectual disability syndrome

ORPHA: 901031 Treatment Available

Available Treatments (1)

DrugFormStatusCountriesLead Time
gabapentin
Oral capsule 100mg, 300mg, 400mg; Oral tablet 600mg, 800mg; Oral solution 250mg/5mLFDA Approved, EMA Approved113d

Clinical Presentation

Signs and symptoms associated with Charcot-Marie-tooth disease-deafness-intellectual disability syndrome, sourced from HPO and Orphanet clinical annotations.

Decreased nerve conduction velocityMild intellectual disabilityDecreased number of large peripheral myelinated nerve fibersDecreased amplitude of sensory action potentialsSensorimotor neuropathyLower limb amyotrophySevere sensorineural hearing impairmentDysarthriaGlobal developmental delayAbsent speechFailure to thrive in infancyPes cavusGait ataxiaAreflexia of lower limbsAbnormality of peripheral nerve conductionDistal sensory impairment of all modalitiesAbsent Achilles reflexImpaired vibration sensation at anklesDistal lower limb amyotrophyIntrinsic hand muscle atrophyDistal upper limb muscle weaknessCalf muscle hypoplasiaFoot dorsiflexor weaknessAmyotrophy of ankle musculatureDistal lower limb muscle weaknessUpper limb amyotrophyRespiratory insufficiencyAreflexia of upper limbsPain

Classification & Codes

Orphanet Code

ORPHA:90103
Charcot-Marie-tooth disease-deafness-intellectual disability syndrome
OrphanetORPHA:90103
Treatments1 drug(s)
Symptoms on record29 signs
Statuspublished

Treatment Summary

Factual Authority
Last Updated3/20/2026
Clinical DataHPO · Orphanet
Drug DataFDA · EMA · CDSCO